Pages that link to "Q40551652"
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The following pages link to Mutant huntingtin directly increases susceptibility of mitochondria to the calcium-induced permeability transition and cytochrome c release (Q40551652):
Displaying 50 items.
- Parkin, PINK1, and DJ-1 form a ubiquitin E3 ligase complex promoting unfolded protein degradation (Q24312713) (← links)
- Rhes, a striatal specific protein, mediates mutant-huntingtin cytotoxicity (Q24317318) (← links)
- Clioquinol down-regulates mutant huntingtin expression in vitro and mitigates pathology in a Huntington's disease mouse model (Q24535603) (← links)
- Tissue transglutaminase overexpression does not modify the disease phenotype of the R6/2 mouse model of Huntington's disease (Q24618141) (← links)
- Mitochondria, calcium and cell death: a deadly triad in neurodegeneration (Q24646020) (← links)
- Mitochondria-associated membranes as hubs for neurodegeneration (Q26770200) (← links)
- Old Things New View: Ascorbic Acid Protects the Brain in Neurodegenerative Disorders (Q26775096) (← links)
- Electron Transport Disturbances and Neurodegeneration: From Albert Szent-Györgyi's Concept (Szeged) till Novel Approaches to Boost Mitochondrial Bioenergetics (Q26795417) (← links)
- Role of cerebral cortex in the neuropathology of Huntington's disease (Q26829211) (← links)
- Iron dysregulation in Huntington's disease (Q26829932) (← links)
- PGC-1α, mitochondrial dysfunction, and Huntington's disease (Q27001671) (← links)
- Mouse models of polyglutamine diseases in therapeutic approaches: review and data table. Part II. (Q27005950) (← links)
- Therapeutic Approaches for Inhibition of Protein Aggregation in Huntington's Disease (Q27022757) (← links)
- Structure and Topology of the Huntingtin 1–17 Membrane Anchor by a Combined Solution and Solid-State NMR Approach (Q27679485) (← links)
- The chicken or the egg: mitochondrial dysfunction as a cause or consequence of toxicity in Huntington's disease (Q28072937) (← links)
- Polyglutamine tract-binding protein-1 dysfunction induces cell death of neurons through mitochondrial stress (Q28267631) (← links)
- Mitochondrial dysfunction and oxidative stress in neurodegenerative diseases (Q28269333) (← links)
- Shaping the role of mitochondria in the pathogenesis of Huntington's disease (Q28384036) (← links)
- Role of oxidative DNA damage in mitochondrial dysfunction and Huntington's disease pathogenesis (Q28386202) (← links)
- Metabolism in HD: still a relevant mechanism? (Q28394301) (← links)
- Inhibition of mitochondrial protein import by mutant huntingtin (Q28394803) (← links)
- Mitochondrial lipids in neurodegeneration (Q28397548) (← links)
- Unbiased gene expression analysis implicates the huntingtin polyglutamine tract in extra-mitochondrial energy metabolism (Q28469280) (← links)
- Heterogeneous nuclear ribonucleoprotein K enhances insulin-induced expression of mitochondrial UCP2 protein (Q28573381) (← links)
- Mitochondrial aconitase is a transglutaminase 2 substrate: transglutamination is a probable mechanism contributing to high-molecular-weight aggregates of aconitase and loss of aconitase activity in Huntington disease brain (Q28580981) (← links)
- 14-3-3theta Protects against Neurotoxicity in a Cellular Parkinson's Disease Model through Inhibition of the Apoptotic Factor Bax (Q28742388) (← links)
- Proteomic analysis of wild-type and mutant huntingtin-associated proteins in mouse brains identifies unique interactions and involvement in protein synthesis (Q30418699) (← links)
- Elucidating a normal function of huntingtin by functional and microarray analysis of huntingtin-null mouse embryonic fibroblasts (Q30441792) (← links)
- N-terminal mutant huntingtin associates with mitochondria and impairs mitochondrial trafficking (Q30486372) (← links)
- PGC-1α rescues Huntington's disease proteotoxicity by preventing oxidative stress and promoting TFEB function. (Q30583566) (← links)
- A role for voltage-dependent anion channel Vdac1 in polyglutamine-mediated neuronal cell death (Q33305438) (← links)
- High-resolution respirometry of fine-needle muscle biopsies in pre-manifest Huntington's disease expansion mutation carriers shows normal mitochondrial respiratory function. (Q33562672) (← links)
- Mitochondrial matters of the brain: the role in Huntington's disease (Q33580327) (← links)
- Potent inhibition of huntingtin aggregation and cytotoxicity by a disulfide bond-free single-domain intracellular antibody (Q33580733) (← links)
- Angiotensins and Huntington's Disease: A Study on Immortalized Progenitor Striatal Cell Lines (Q33720370) (← links)
- Disturbed Ca2 signaling and apoptosis of medium spiny neurons in Huntington's disease. (Q33850154) (← links)
- Huntingtin protein is essential for mitochondrial metabolism, bioenergetics and structure in murine embryonic stem cells (Q33945927) (← links)
- Impairment of PGC-1alpha expression, neuropathology and hepatic steatosis in a transgenic mouse model of Huntington's disease following chronic energy deprivation (Q34042260) (← links)
- Mitochondrial calcium uptake capacity as a therapeutic target in the R6/2 mouse model of Huntington's disease (Q34046887) (← links)
- Metabolic State Determines Sensitivity to Cellular Stress in Huntington Disease: Normalization by Activation of PPARγ (Q34140579) (← links)
- Increased mitochondrial fission and neuronal dysfunction in Huntington's disease: implications for molecular inhibitors of excessive mitochondrial fission (Q34313991) (← links)
- Huntington's disease and its therapeutic target genes: a global functional profile based on the HD Research Crossroads database (Q34319766) (← links)
- Altered Ca(2 ) signaling in skeletal muscle fibers of the R6/2 mouse, a model of Huntington's disease (Q34409630) (← links)
- Therapeutic approaches to preventing cell death in Huntington disease (Q34411338) (← links)
- Mitochondrial dysfunction and apoptosis underlie the pathogenic process in alpha-B-crystallin desmin-related cardiomyopathy (Q34442070) (← links)
- Involvement of mitochondrial complex II defects in neuronal death produced by N-terminus fragment of mutated huntingtin (Q34483577) (← links)
- Mitochondrial fission and cristae disruption increase the response of cell models of Huntington's disease to apoptotic stimuli (Q34605764) (← links)
- Abnormal mitochondrial dynamics, mitochondrial loss and mutant huntingtin oligomers in Huntington's disease: implications for selective neuronal damage (Q34627072) (← links)
- Mutant huntingtin binds the mitochondrial fission GTPase dynamin-related protein-1 and increases its enzymatic activity (Q34634421) (← links)
- A novel transferrin/TfR2-mediated mitochondrial iron transport system is disrupted in Parkinson's disease (Q34658144) (← links)