Prion protein transgenes and the neuropathology in prion diseases (Q40537035)

21 September 2017

1 reference

title

Prion protein transgenes and the neuropathology in prion diseases (English)

1 reference

21 September 2017

0 references

2

Prusiner SB

1 reference

21 September 2017

1

DeArmond SJ

1 reference

21 September 2017

publication date

1 January 1995

1 reference

21 September 2017

1 reference

21 September 2017

volume

5

1 reference

21 September 2017

issue

1

1 reference

21 September 2017

page(s)

77-89

1 reference

Each caveola contains multiple glycosyl-phosphatidylinositol-anchored membrane proteins

21 September 2017

cites work

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

A glycolipid-anchored prion protein is endocytosed via clathrin-coated pits.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Scrapie and cellular prion proteins differ in their kinetics of synthesis and topology in cultured cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Proteinase-resistant prion protein accumulation in Syrian hamster brain correlates with regional pathology and scrapie infectivity

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

The neurochemistry of prion diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Structural studies of the scrapie prion protein using mass spectrometry and amino acid sequencing.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Scrapie prions aggregate to form amyloid-like birefringent rods

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Secondary structure analysis of the scrapie-associated protein PrP 27-30 in water by infrared spectroscopy

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Perturbation of the secondary structure of the scrapie prion protein under conditions that alter infectivity

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Further purification and characterization of scrapie prions

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Identification of a protein that purifies with the scrapie prion

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Molecular cloning of a human prion protein cDNA

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Linkage of the Indiana kindred of Gerstmann-Sträussler-Scheinker disease to the prion protein gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Inherited prion disease with 144 base pair gene insertion. 1. Genealogical and molecular studies

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Analysis of the prion protein gene in thalamic dementia

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Proposed three-dimensional structure for the cellular prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Predicted alpha-helical regions of the prion protein when synthesized as peptides form amyloid

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Mutant prion proteins in Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Fatal familial insomnia: a second kindred with mutation of prion protein gene at codon 178

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Fatal familial insomnia and familial Creutzfeldt-Jakob disease: disease phenotype determined by a DNA polymorphism

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Human spongiform encephalopathy: the National Institutes of Health series of 300 cases of experimentally transmitted disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Spontaneous neurodegeneration in transgenic mice with mutant prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Serial transmission in rodents of neurodegeneration from transgenic mice expressing mutant prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Mice devoid of PrP are resistant to scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Ablation of the prion protein (PrP) gene in mice prevents scrapie and facilitates production of anti-PrP antibodies

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Transgenic mice expressing hamster prion protein produce species-specific scrapie infectivity and amyloid plaques.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Identification of prion amyloid filaments in scrapie-infected brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Changes in the localization of brain prion proteins during scrapie infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Replication of distinct scrapie prion isolates is region specific in brains of transgenic mice and hamsters

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Three scrapie prion isolates exhibit different accumulation patterns of the prion protein scrapie isoform

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Propagation of prions with artificial properties in transgenic mice expressing chimeric PrP genes.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Transmission of Creutzfeldt-Jakob disease from humans to transgenic mice expressing chimeric human-mouse prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Regional mapping of prion proteins in brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Structural clues to prion replication

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Distinct prion proteins in short and long scrapie incubation period mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Identification of a gene which controls the incubation period of some strains of scrapie agent in mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Paradoxical shortening of scrapie incubation times by expression of prion protein transgenes derived from long incubation period mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Prion isolate specified allotypic interactions between the cellular and scrapie prion proteins in congenic and transgenic mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Degeneration of skeletal muscle, peripheral nerves, and the central nervous system in transgenic mice overexpressing wild-type prion proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Deletion in prion protein gene in a Moroccan family

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Deletions in the prion protein gene are not associated with CJD.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

"Friendly fire" in medicine: hormones, homografts, and Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Transmissible familial Creutzfeldt-Jakob disease associated with five, seven, and eight extra octapeptide coding repeats in the PRNP gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

An in-frame insertion in the prion protein gene in familial Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Pro----leu change at position 102 of prion protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Sträussler-Scheinker's syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Novel missense variants of prion protein in Creutzfeldt-Jakob disease or Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Familial dementia with PrP-positive amyloid plaques: a variant of Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Mutation in codon 200 of scrapie amyloid protein gene in two clusters of Creutzfeldt-Jakob disease in Slovakia

21 January 2018

1 reference

https://api.crossref.org/works/10.1111/J.1750-3639.1995.TB00579.X

Creutzfeldt-Jakob disease cosegregates with the codon 178Asn PRNP mutation in families of European origin

21 January 2018

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Insertion in prion protein gene in familial Creutzfeldt-Jakob disease

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Creutzfeldt-Jakob disease and kuru patients lack a mutation consistently found in the Gerstmann-Sträussler-Scheinker syndrome

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Host-genotype and agent effects in scrapie incubation: Change in allelic interaction with different strains of agent

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

New mutation in scrapie amyloid precursor gene (at codon 178) in Finnish Creutzfeldt-Jakob kindred

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Linkage of prion protein and scrapie incubation time genes

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Precise targeting of the pathology of the sialoglycoprotein, PrP, and vacuolar degeneration in mouse scrapie

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Mutation of the prion protein in Libyan Jews with Creutzfeldt-Jakob disease

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Fatal familial insomnia, a prion disease with a mutation at codon 178 of the prion protein gene

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

A new point mutation in the prion protein gene at codon 210 in Creutzfeldt-Jakob disease

1 reference

11 October 2022

https://opencitations.net/index/coci/api/v1/references/10.1111/J.1750-3639.1995.TB00579.X

Identifiers

DOI

10.1111/J.1750-3639.1995.TB00579.X

1 reference

21 September 2017

1 reference