Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo (Q35902688)

11 August 2017

Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo (English)

1 reference

11 August 2017

Thoene JG

1

1 reference

11 August 2017

Oshima RG

2

1 reference

11 August 2017

Crawhall JC

3

1 reference

11 August 2017

Olson DL

4

1 reference

11 August 2017

Schneider JA

5

1 reference

11 August 2017

language of work or name

English

0 references

publication date

1 July 1976

1 reference

Journal of Clinical Investigation

11 August 2017

1 reference

11 August 2017

58

1 reference

11 August 2017

1

1 reference

11 August 2017

180-189

1 reference

Protein measurement with the Folin phenol reagent

11 August 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Analytical separations by highvoltage paper electrophoresis. Amino acids in protein hydrolysates

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Plaque formation and isolation of pure lines with poliomyelitis viruses

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

The fate of peptides pinocytosed by macrophages in vitro

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Cystinosis: Selective Induction of Vacuolation in Fibroblasts by L-Cysteine-D-Penicillamine Disulfide

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Decrease in Free Cystine Content of Cultured Cystinotic Fibroblasts by Ascorbic Acid

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Rifampicin and cysteamine protect against the mushroom toxin phalloidin.

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

The mechanism of disulphide reduction by mitochondria

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Use of dithiothreitol to correct cystine storage in cultured cystinotic fibroblasts

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Effect of penicillamine (a vitamin B6 antagonist) on pyridoxal enzymes

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Homocystinuria due to cystathionine synthase deficiency. Studies of nitrogen balance and sulfur excretion

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

The effect of the convulsant 3-mercaptopropionic acid on enzymes of the gamma-aminobutyrate system in the rat cerebral cortex

11 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=333169

Increased free-cystine content of fibroblasts cultured from patients with cystinosis

24 September 2018

1 reference

12 December 2020

The Pharmacology of Radioprotectant Chemicals: General Pharmacology of β-Mercaptoethylamine

1 reference

12 December 2020

CYSTINURIA: EFFECT OF D-PENICILLAMINE ON PLASMA AND URINARY CYSTINE CONCENTRATIONS

1 reference

12 December 2020

Blood and urine sulfhydryl and disulfide levels after large doses of betamercaptoethylamine (MEA) or cystamine

1 reference

12 December 2020

On the mode of action of x-ray protective agents. III. The enzymatic reduction of disulfides

1 reference

12 December 2020

A simple method for the preparation of protoporphyrin from washed erythrocytes

1 reference

12 December 2020

Enzymatic degradation and resynthesis of coenzyme A

1 reference

12 December 2020

Successful treatment of severe paracetamol overdosage with cysteamine

1 reference

12 December 2020

Binding assays for amino acids. The utilization of a cystine binding protein from Escherichia coli for the determination of acid-soluble cystine in small physiological samples

1 reference

12 December 2020

Measurement of intracellular amino acids in cultured skin fibroblasts. The effect of storage on cystine recovery and evaluation of three methods of cell preparation

1 reference

12 December 2020

Acetaminophen-induced hepatic injury: protective role of glutathione in man and rationale for therapy.

1 reference

12 December 2020

Single-column system for accelerated amino acid analysis of physiological fluids using five lithium buffers

1 reference

12 December 2020

Cystine, cysteine, and glutathione metabolism in normal and cystinotic fibroblasts in vitro, and in cultured normal amniotic fluid cells

1 reference

12 December 2020

Cystinosis: Therapeutic implications of in vitro studies of cultured fibroblasts

1 reference

12 December 2020

Cystinosis. Plasma cystine and cysteine concentrations and the effect of D-penicillamine and dietary treatment

1 reference

12 December 2020

Identifiers

DOI

10.1172/JCI108448

1 reference

11 August 2017

1 reference

11 August 2017

PubMed publication ID

932205

1 reference