In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis (Q35089820)

6 August 2017

title

In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis (English)

1 reference

6 August 2017

9

Massimo Zeviani

1 reference

6 August 2017

8

Costanza Lamperti

1 reference

6 August 2017

6

Gigliola Fagiolari

1 reference

6 August 2017

5

Maurizio Moggio

1 reference

6 August 2017

1

Carlo Viscomi

1 reference

6 August 2017

Emanuela Bottani

2

1 reference

6 August 2017

Gabriele Civiletto

series ordinal

3

1 reference

6 August 2017

Raffaele Cerutti

series ordinal

4

1 reference

6 August 2017

Eric A Schon

series ordinal

7

1 reference

6 August 2017

publication date

1 July 2011

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6 August 2017

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6 August 2017

volume

14

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6 August 2017

issue

1

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6 August 2017

page(s)

80-90

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AMP-activated protein kinase and its downstream transcriptional pathways

6 August 2017

cites work

1 reference

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8 July 2018

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Mitochondrial energetics and therapeutics

8 July 2018

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Calmodulin-dependent protein kinase kinase-beta activates AMPK without forming a stable complex: synergistic effects of Ca2 and AMP.

8 July 2018

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Analysis of mouse models of cytochrome c oxidase deficiency owing to mutations in Sco2

8 July 2018

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Energetics, epigenetics, mitochondrial genetics

8 July 2018

1 reference

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Rhabdomyolysis associated with fibrate therapy: review of 76 published cases and a new case report

8 July 2018

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AMPK in Health and Disease

8 July 2018

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PPAR{delta} agonism activates fatty acid oxidation via PGC-1{alpha} but does not increase mitochondrial gene expression and function

8 July 2018

1 reference

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Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1.

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

PGC-1alpha/beta induced expression partially compensates for respiratory chain defects in cells from patients with mitochondrial disorders.

8 July 2018

1 reference

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AMPK regulates energy expenditure by modulating NAD metabolism and SIRT1 activity

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Early-onset liver mtDNA depletion and late-onset proteinuric nephropathy in Mpv17 knockout mice

8 July 2018

1 reference

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RETRACTED: Activation of the PPAR/PGC-1alpha pathway prevents a bioenergetic deficit and effectively improves a mitochondrial myopathy phenotype

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

AMP-activated protein kinase (AMPK) action in skeletal muscle via direct phosphorylation of PGC-1alpha

8 July 2018

1 reference

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Metabolic control of muscle mitochondrial function and fatty acid oxidation through SIRT1/PGC-1alpha

8 July 2018

1 reference

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Resveratrol improves mitochondrial function and protects against metabolic disease by activating SIRT1 and PGC-1alpha

8 July 2018

1 reference

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Peroxisome proliferator-activated receptor gamma coactivator 1 coactivators, energy homeostasis, and metabolism

8 July 2018

1 reference

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PPAR delta: a dagger in the heart of the metabolic syndrome

8 July 2018

1 reference

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Sorting out the roles of PPAR alpha in energy metabolism and vascular homeostasis

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

A mitochondrial paradigm of metabolic and degenerative diseases, aging, and cancer: a dawn for evolutionary medicine

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Biogenesis of cytochrome c oxidase

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Dual and pan-peroxisome proliferator-activated receptors (PPAR) co-agonism: the bezafibrate lessons

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Novel mutations in COX15 in a long surviving Leigh syndrome patient with cytochrome c oxidase deficiency

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

8 July 2018

Mitochondrial disorders

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Regulation of muscle fiber type and running endurance by PPARdelta

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Transcriptional regulatory circuits controlling mitochondrial biogenesis and function

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Mutations in COX15 produce a defect in the mitochondrial heme biosynthetic pathway, causing early-onset fatal hypertrophic cardiomyopathy

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Transcriptional co-activator PGC-1 alpha drives the formation of slow-twitch muscle fibres

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Fatal infantile cardioencephalomyopathy with COX deficiency and mutations in SCO2, a COX assembly gene

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

AICA riboside increases AMP-activated protein kinase, fatty acid oxidation, and glucose uptake in rat muscle

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

5-aminoimidazole-4-carboxamide ribonucleoside. A specific method for activating AMP-activated protein kinase in intact cells?

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Activation of peroxisome proliferator-activated receptor pathway stimulates the mitochondrial respiratory chain and can correct deficiencies in patients' cells lacking its components

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Clinical and molecular findings in children with complex I deficiency

27 September 2018

1 reference

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Characterization of SURF-1 expression and Surf-1p function in normal and disease conditions

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Peroxisome proliferator-activated receptor delta controls muscle development and oxidative capability

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3130927

Increased longevity and refractoriness to Ca(2 )-dependent neurodegeneration in Surf1 knockout mice

16 November 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21723506

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Bezafibrates cause moderate, reversible impairment in renal function in patients without prior renal disease

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21723506

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Cytochemistry and immunocytochemistry of mitochondria in tissue sections

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21723506

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1016/J.CMET.2011.04.011

1 reference

6 August 2017

1 reference

6 August 2017

1 reference