The mitochondrial complex I activity is reduced in cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function (Q34489613)

2 August 2017

title

The mitochondrial complex I activity is reduced in cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function (English)

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2 August 2017

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transmembrane protein

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Tomás A Santa-Coloma

9

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author name string

Angel G Valdivieso

1

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2 August 2017

Mariángeles Clauzure

2

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2 August 2017

María C Marín

3

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2 August 2017

Guillermo L Taminelli

4

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2 August 2017

María M Massip Copiz

5

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2 August 2017

Francisco Sánchez

6

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2 August 2017

Gustavo Schulman

7

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2 August 2017

María L Teiber

8

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2 August 2017

language of work or name

English

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publication date

21 November 2012

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2 August 2017

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2 August 2017

volume

7

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2 August 2017

issue

11

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2 August 2017

page(s)

e48059

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Creative Commons Attribution 4.0 International

2 August 2017

copyright license

start time

21 November 2012

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April 2022 Public Data File from Crossref

copyright status

copyrighted

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describes a project that uses

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3504030/fullTextXML

inferred from PubMed Central ID database lookup

cites work

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The expression of the mitochondrial gene MT-ND4 is downregulated in cystic fibrosis

6 July 2018

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Chloride transporting capability of Calu-3 epithelia following persistent knockdown of the cystic fibrosis transmembrane conductance regulator, CFTR.

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6 July 2018

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Structural organization of mitochondrial human complex I: role of the ND4 and ND5 mitochondria-encoded subunits and interaction with prohibitin

6 July 2018

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6 July 2018

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Identification of a novel mitochondrial protein (“mitoNEET”) cross-linked specifically by a thiazolidinedione photoprobe

6 July 2018

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Plasma membrane CFTR regulates RANTES expression via its C-terminal PDZ-interacting motif

6 July 2018

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Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion.

6 July 2018

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6 July 2018

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6 July 2018

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6 July 2018

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6 July 2018

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Mitochondrial NADH dehydrogenase in cystic fibrosis: enzyme kinetics in cultured fibroblasts.

6 July 2018

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Cystic fibrosis--a lethal exocrinopathy with altered mitochondrial calcium metabolism

6 July 2018

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The mitochondrial electron transport and oxidative phosphorylation system

6 July 2018

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6 July 2018

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Evidence for a mitochondrial lesion in cystic fibrosis

6 July 2018

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Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

6 July 2018

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Development and biological applications of chloride-sensitive fluorescent indicators

6 July 2018

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Menadione partially restores NADH-oxidation and ATP-synthesis in complex I deficient fibroblasts

6 July 2018

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Electron transfer properties of NADH:ubiquinone reductase in the ND1/3460 and the ND4/11778 mutations of the Leber hereditary optic neuroretinopathy (LHON)

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3504030

A Cystic Fibrosis Bronchial Epithelial Cell Line: Immortalization by Adeno-12-SV40 Infection

6 July 2018

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Blue native electrophoresis for isolation of membrane protein complexes in enzymatically active form

6 July 2018

1 reference

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Expression and characterization of the cystic fibrosis transmembrane conductance regulator.

6 July 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3504030

Defective regulation of outwardly rectifying Cl- channels by protein kinase A corrected by insertion of CFTR

6 July 2018

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Antisense oligodeoxynucleotides to the cystic fibrosis transmembrane conductance regulator inhibit cAMP-activated but not calcium-activated chloride currents

6 July 2018

1 reference

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Regulation of CFTR expression and function during differentiation of intestinal epithelial cells

6 July 2018

1 reference

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Cystic fibrosis transmembrane conductance regulator: a chloride channel with novel regulation

6 July 2018

1 reference

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Mitochondrial calcium uptake and oxygen consumption in cystic fibrosis

6 July 2018

1 reference

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Mitrochondrial NADH dehydrogenase in cystic fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3504030

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

6 July 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Analysis of CFTR Folding and Degradation in Transiently Transfected Cells

21 January 2018

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https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

CISD1 codifies a mitochondrial protein upregulated by the CFTR channel.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Binding of reduced nicotinamide adenine dinucleotide phosphate destabilizes the iron−sulfur clusters of human mitoNEET.

21 January 2018

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Chapter 13 Localization and function of the 2Fe-2S outer mitochondrial membrane protein mitoNEET.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Functional alterations of the mitochondrially encoded ND4 subunit associated with Leber's hereditary optic neuropathy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Quantification of muscle mitochondrial oxidative phosphorylation enzymes via histochemical staining of blue native polyacrylamide gels

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Microplate-based kinetic method for assay of mitochondrial NADH-- and succinate--cytochrome c reductase activities.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Effects of rotenone and pyridaben on complex I electron transfer and on mitochondrial nitric oxide synthase functional activity

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Measurement of cystic fibrosis transmembrane conductance regulator activity using fluorescence spectrophotometry.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Mitochondrial complex I defect induces ROS release and degeneration in trabecular meshwork cells of POAG patients: protection by antioxidants

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Electron transport complex I is required for CD8 T cell function.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

'Secondary' 4216/ND1 and 13708/ND5 Leber's hereditary optic neuropathy mitochondrial DNA mutations do not further impair in vivo mitochondrial oxidative metabolism when associated with the 11778/ND4 mitochondrial DNA mutation

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3504030

Episomal expression of wild-type CFTR corrects cAMP-dependent chloride transport in respiratory epithelial cells

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3504030

Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells

27 October 2018

1 reference

https://api.crossref.org/works/10.1371/JOURNAL.PONE.0048059

Mitochondrial dysfunction, energy expenditure, and cystic fibrosis

21 January 2018

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12 December 2020

Skeletal muscle weakness, exercise tolerance and physical activity in adults with cystic fibrosis

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12 December 2020

The calcium abnormality in cystic fibrosis mitochondria: relative role of respiration and ATP hydrolysis

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12 December 2020

Population variation of common cystic fibrosis mutations. The Cystic Fibrosis Genetic Analysis Consortium

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12 December 2020

10.1371/JOURNAL.PONE.0048059

Identifiers

DOI

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2 August 2017

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2 August 2017

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