Expanding our understanding of polyglutamine diseases through mouse models (Q33792953)

29 July 2017

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title

Expanding our understanding of polyglutamine diseases through mouse models (English)

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29 July 2017

3

Zoghbi HY

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29 July 2017

Lin X

1

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29 July 2017

Cummings CJ

series ordinal

2

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29 July 2017

language of work or name

English

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publication date

1 November 1999

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29 July 2017

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29 July 2017

volume

24

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29 July 2017

issue

3

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29 July 2017

page(s)

499-502

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SCA1 transgenic mice: A model for neurodegeneration caused by an expanded CAG trinucleotide repeat

29 July 2017

cites work

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https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Purkinje cell expression of a mutant allele of SCA1 in transgenic mice leads to disparate effects on motor behaviors, followed by a progressive cerebellar dysfunction and histological alterations.

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https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1.

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https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

A YAC mouse model for Huntington's disease with full-length mutant huntingtin, cytoplasmic toxicity, and selective striatal neurodegeneration.

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Expression of ataxin-2 in brains from normal individuals and patients with Alzheimer's disease and spinocerebellar ataxia 2.

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Expanded polyglutamine in the Machado-Joseph disease protein induces cell death in vitro and in vivo

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https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Abundant expression and cytoplasmic aggregations of [alpha]1A voltage-dependent calcium channel protein associated with neurodegeneration in spinocerebellar ataxia type 6

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Ataxin-1 nuclear localization and aggregation: role in polyglutamine-induced disease in SCA1 transgenic mice

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Inhibition of caspase-1 slows disease progression in a mouse model of Huntington's disease

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Ectopically Expressed CAG Repeats Cause Intranuclear Inclusions and a Progressive Late Onset Neurological Phenotype in the Mouse

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Protein fate in neurodegenerative proteinopathies: polyglutamine diseases join the (mis)fold

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Behavioural abnormalities and selective neuronal loss in HD transgenic mice expressing mutated full-length HD cDNA.

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

A Huntington's disease CAG expansion at the murine Hdh locus is unstable and associated with behavioural abnormalities in mice

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

Impaired synaptic plasticity in mice carrying the Huntington's disease mutation

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

1 reference

7 January 2021

Huntingtin is required for neurogenesis and is not impaired by the Huntington's disease CAG expansion

1 reference

https://api.crossref.org/works/10.1016/S0896-6273(00)81104-6

7 January 2021

10.1016/S0896-6273(00)81104-6

Identifiers

DOI

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29 July 2017

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