Inherited long QT syndromes: a paradigm for understanding arrhythmogenesis (Q33145216)

22 July 2017

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title

Inherited long QT syndromes: a paradigm for understanding arrhythmogenesis (English)

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22 July 2017

Roden DM

1

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22 July 2017

Spooner PM

series ordinal

2

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22 July 2017

publication date

1 December 1999

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Journal of Cardiovascular Electrophysiology

22 July 2017

published in

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22 July 2017

volume

10

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22 July 2017

issue

12

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22 July 2017

page(s)

1664-1683

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Prolongation of the QT interval and the sudden infant death syndrome.

22 July 2017

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Two Isoforms of the Mouse Ether-a-go-go –Related Gene Coassemble to Form Channels With Properties Similar to the Rapidly Activating Component of the Cardiac Delayed Rectifier K Current

21 January 2018

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Electrophysiological Characterization of an Alternatively Processed ERG K Channel in Mouse and Human Hearts

21 January 2018

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Mutations in a dominant-negative isoform correlate with phenotype in inherited cardiac arrhythmias

21 January 2018

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A novel mutation in the potassium channel gene KVLQT1 causes the Jervell and Lange-Nielsen cardioauditory syndrome

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Molecular basis of the long-QT syndrome associated with deafness

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Sex hormones prolong the QT interval and downregulate potassium channel expression in the rabbit heart

21 January 2018

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A multivalent PDZ-domain protein assembles signalling complexes in a G-protein-coupled cascade

21 January 2018

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Cloning and expression of a novel K channel regulatory protein, KChAP

21 January 2018

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21 January 2018

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21 January 2018

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Human KVLQT1 gene shows tissue-specific imprinting and encompasses Beckwith-Wiedemann syndrome chromosomal rearrangements.

21 January 2018

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Long QT syndrome associated with syndactyly identified in females

21 January 2018

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Lidocaine block of LQT-3 mutant human Na channels

21 January 2018

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A family of sulfonylurea receptors determines the pharmacological properties of ATP-sensitive K channels

21 January 2018

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A view of sur/KIR6.X, KATP channels

21 January 2018

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Role of external Ca2 and K in gating of cardiac delayed rectifier K currents

21 January 2018

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Rapid inactivation determines the rectification and [K ]o dependence of the rapid component of the delayed rectifier K current in cardiac cells.

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Genomic organization and mutational analysis of HERG, a gene responsible for familial long QT syndrome

21 January 2018

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21 January 2018

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21 January 2018

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Precordial QT interval dispersion as a marker of torsade de pointes. Disparate effects of class Ia antiarrhythmic drugs and amiodarone

21 January 2018

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Amiodarone and torsade de pointes

21 January 2018

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Beat-to-beat QT interval variability: novel evidence for repolarization lability in ischemic and nonischemic dilated cardiomyopathy.

21 January 2018

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Early afterdepolarizations: mechanism of induction and block. A role for L-type Ca2 current

21 January 2018

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The steady state TTX-sensitive ("window") sodium current in cardiac Purkinje fibres

21 January 2018

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21 January 2018

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21 January 2018

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T-type Ca2 channels and pharmacological blockade: potential pathophysiological relevance

21 January 2018

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Microbubbles targeted to intercellular adhesion molecule-1 bind to activated coronary artery endothelial cells

21 January 2018

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21 January 2018

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21 January 2018

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Inhibition of cardiac delayed rectifier K current by overexpression of the long-QT syndrome HERG G628S mutation in transgenic mice

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Disturbed connexin43 gap junction distribution correlates with the location of reentrant circuits in the epicardial border zone of healing canine infarcts that cause ventricular tachycardia.

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New insights into myocardial arrhythmogenesis: distribution of gap-junctional coupling in normal, ischaemic and hypertrophied human hearts

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21 January 2018

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Calcium-dependent inactivation of the dihydropyridine-sensitive calcium channels in GH3 cells

21 January 2018

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Calcium-activated chloride current in rabbit ventricular myocytes

21 January 2018

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21 January 2018

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21 January 2018

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DOI

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22 July 2017

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