(Q34016471)

English

CFTR with a partially deleted R domain corrects the cystic fibrosis chloride transport defect in human airway epithelia in vitro and in mouse nasal mucosa in vivo

scientific article

In more languages

default for all languages

No label defined

No description defined

Statements

scholarly article

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

CFTR with a partially deleted R domain corrects the cystic fibrosis chloride transport defect in human airway epithelia in vitro and in mouse nasal mucosa in vivo (English)

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

cystic fibrosis

0 references

author name string

Lynda S Ostedgaard

1

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Joseph Zabner

2

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Daniel W Vermeer

3

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Tatiana Rokhlina

4

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Philip H Karp

5

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Arlene A Stecenko

6

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Christoph Randak

7

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Michael J Welsh

8

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

language of work or name

0 references

publication date

19 February 2002

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Proceedings of the National Academy of Sciences of the United States of America

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

99

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

5

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

3093-3098

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Adeno-associated virus type 6 (AAV6) vectors mediate efficient transduction of airway epithelial cells in mouse lungs compared to that of AAV2 vectors

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Non-specific activation of the epithelial sodium channel by the CFTR chloride channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Binding of adeno-associated virus type 5 to 2,3-linked sialic acid is required for gene transfer

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Regulation of the cystic fibrosis transmembrane conductance regulator Cl- channel by its R domain

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Gene therapy vectors based on adeno-associated virus: characteristics and applications to acquired and inherited diseases (review).

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Severed channels probe regulation of gating of cystic fibrosis transmembrane conductance regulator by its cytoplasmic domains

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Adeno-associated viral vectors as gene delivery vehicles

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

A functional R domain from cystic fibrosis transmembrane conductance regulator is predominantly unstructured in solution

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Adeno-associated virus type 5 (AAV5) but not AAV2 binds to the apical surfaces of airway epithelia and facilitates gene transfer

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Conformation, independent of charge, in the R domain affects cystic fibrosis transmembrane conductance regulator channel openings

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Gene transfer for cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Structure and function of the CFTR chloride channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Efficient expression of CFTR function with adeno-associated virus vectors that carry shortened CFTR genes

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Incorporation of adenovirus in calcium phosphate precipitates enhances gene transfer to airway epithelia in vitro and in vivo

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Membrane-Associated Heparan Sulfate Proteoglycan Is a Receptor for Adeno-Associated Virus Type 2 Virions

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Function of the R Domain in the Cystic Fibrosis Transmembrane Conductance Regulator Chloride Channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Quantitative analysis of the packaging capacity of recombinant adeno-associated virus

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Human airway ion transport. Part one.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Regulation of the cystic fibrosis transmembrane conductance regulator Cl- channel by negative charge in the R domain.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

A mouse model for the delta F508 allele of cystic fibrosis.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Normalization of raised sodium absorption and raised calcium-mediated chloride secretion by adenovirus-mediated expression of cystic fibrosis transmembrane conductance regulator in primary human cystic fibrosis airway epithelial cells

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

The two nucleotide-binding domains of cystic fibrosis transmembrane conductance regulator (CFTR) have distinct functions in controlling channel activity

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Effect of deletion mutations on the function of CFTR chloride channels

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Expression of full-length and truncated dystrophin mini-genes in transgenic mdx mice

1 reference

https://api.crossref.org/works/10.1073/PNAS.261714599

21 January 2018

Basolateral localization of fiber receptors limits adenovirus infection from the apical surface of airway epithelia

1 reference

https://api.crossref.org/works/10.1073/PNAS.261714599

21 January 2018

Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro.

1 reference

https://api.crossref.org/works/10.1073/PNAS.261714599

21 January 2018

Stimulation of CFTR activity by its phosphorylated R domain

1 reference

https://api.crossref.org/works/10.1073/PNAS.261714599

21 January 2018

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

1 reference

https://api.crossref.org/works/10.1073/PNAS.261714599

21 January 2018

Characterization of 19 disease-associated missense mutations in the regulatory domain of the cystic fibrosis transmembrane conductance regulator

1 reference

https://api.crossref.org/works/10.1073/PNAS.261714599

21 January 2018

Stimulatory and Inhibitory Functions of the R Domain on CFTR Chloride Channel.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

CFTR is a conductance regulator as well as a chloride channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

Control of CFTR channel gating by phosphorylation and nucleotide hydrolysis.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

CFTR activation: additive effects of stimulatory and inhibitory phosphorylation sites in the R domain

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

Expression of the cystic fibrosis transmembrane conductance regulator from a novel adeno-associated virus promoter

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

Gene therapy for cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Functional characterization of the CFTR R domain using CFTR/MDR1 hybrid and deletion constructs

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Effect of Deleting the R Domain on CFTR-Generated Chloride Channels

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Processing of CFTR bearing the P574H mutation differs from wild-type and deltaF508-CFTR

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Removal of multiple arginine-framed trafficking signals overcomes misprocessing of delta F508 CFTR present in most patients with cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Gene therapy for cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis transmembrane conductance regulator Cl- channels with R domain deletions and translocations show phosphorylation-dependent and -independent activity

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1073/PNAS.261714599

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

2002PNAS...99.3093O

0 references

PMC publication ID

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

ResearchGate publication ID

0 references

Sitelinks

Wikipedia(0 entries)

Wikibooks(0 entries)

Wikinews(0 entries)

Wikiquote(0 entries)

Wikisource(0 entries)

Wikiversity(0 entries)

Wikivoyage(0 entries)

Wiktionary(0 entries)

Multilingual sites(0 entries)

Retrieved from "https://www.wikidata.org/w/index.php?title=Q34016471&oldid=1952214626"