(Q28510933)

25 January 2017

title

Loss of alpha-hemoglobin-stabilizing protein impairs erythropoiesis and exacerbates beta-thalassemia (English)

1 reference

Eukaryotic translation initiation factor 2-alpha kinase 2

25 January 2017

main subject

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ORCID Public Data File 2021

GOA release 2020-03-11

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1 reference

author name string

Yi Kong

1

1 reference

25 January 2017

Suiping Zhou

2

1 reference

25 January 2017

Anthony J. Kihm

3

1 reference

25 January 2017

Anne M. Katein

4

1 reference

25 January 2017

Xiang Yu

5

1 reference

25 January 2017

David A. Gell

6

1 reference

25 January 2017

Joel P. Mackay

7

1 reference

25 January 2017

Kazuhiko Adachi

8

1 reference

25 January 2017

Linda Foster-Brown

9

1 reference

25 January 2017

Calvert S. Louden

10

1 reference

25 January 2017

Andrew J. Gow

11

1 reference

25 January 2017

Mitchell J. Weiss

12

1 reference

25 January 2017

language of work or name

English

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publication date

1 November 2004

1 reference

Journal of Clinical Investigation

25 January 2017

published in

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25 January 2017

volume

114

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25 January 2017

issue

10

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25 January 2017

page(s)

1457–1466

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Heme positively regulates the expression of beta-globin at the locus control region via the transcriptional factor Bach1 in erythroid cells

25 January 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

An abundant erythroid protein that stabilizes free alpha-haemoglobin

19 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Heme-regulated eIF2alpha kinase (HRI) is required for translational regulation and survival of erythroid precursors in iron deficiency

19 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

A mouse model for beta 0-thalassemia

19 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Evaluation of alpha hemoglobin stabilizing protein (AHSP) as a genetic modifier in patients with beta thalassemia.

19 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Biophysical characterization of the alpha-globin binding protein alpha-hemoglobin stabilizing protein

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Pathophysiology of thalassemia

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Ineffective erythropoiesis in Stat5a(-/-)5b(-/-) mice due to decreased survival of early erythroblasts

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Phenotype-genotype relationships in monogenic disease: lessons from the thalassaemias.

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Posttranslational quality control: folding, refolding, and degrading proteins.

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

The oxyhemoglobin reaction of nitric oxide

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Hematopoietic commitment during embryonic stem cell differentiation in culture

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Effect of excess alpha-hemoglobin chains on cellular and membrane oxidation in model beta-thalassemic erythrocytes

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Hemoglobin synthesis in beta-thalassemia: the properties of the free alpha-chains

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Thalassemia: The consequences of unbalanced hemoglobin synthesis

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Beta Thalassemia and Translation of Globin Messenger RNA

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Differing erythrocyte membrane skeletal protein defects in alpha and beta thalassemia

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Oxidative denaturation of red blood cells in thalassemia

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

The role of membrane skeletal-associated alpha-globin in the pathophysiology of beta-thalassemia

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Purification and characterisation of prostaglandin endoperoxide synthetase from sheep vesicular glands

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Molecular mechanism of AHSP-mediated stabilization of alpha-hemoglobin

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Enhancement by Ubiquitin Aldehyde of Proteolysis of Hemoglobin α‐Subunits in β‐Thalassemic Hemolysatesa

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Inclusion-body beta-thalassemia trait. A form of beta thalassemia producing clinical manifestations in simple heterozygotes.

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Characterization and comparison of the red blood cell membrane damage in severe human alpha- and beta-thalassemia

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Excess α Chain Synthesis Relative to β Chain Synthesis in Thalassaemia Major and Minor

2 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Expression of alpha-hemoglobin stabilizing protein gene during human erythropoiesis

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Differential regulatory and compensatory responses in hematopoiesis/erythropoiesis in alpha- and beta-globin hemizygous mice

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Analysis of protein carbonyls with 2,4-dinitrophenyl hydrazine and its antibodies by immunoblot in two-dimensional gel electrophoresis

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=525742

Peptide analysis of the inclusions of erythroid cells in β-thalassemia

27 November 2018

1 reference

12 December 2020

Evidence for soluble a chains as intermediates in hemoglobin synthesis in the rabbit reticulocyte

1 reference

12 December 2020

The control of hemoglobin synthesis

1 reference

12 December 2020

Chromosomal and Cytoplasmic Regulation of Haemoglobin Synthesis

1 reference

12 December 2020

Intracellular Loss of Free α Chains in β Thalassaemia

1 reference

12 December 2020

The pattern of disordered haemoglobin synthesis in homozygous and heterozygous beta-thalassaemia

1 reference

12 December 2020

Regulation of hemoglobin synthesis. Equal rates of translation and termination of - and -globin chains

1 reference

12 December 2020

Increased sensitivity of isolated alpha subunits of normal human hemoglobin to oxidative damage and crosslinkage with spectrin

1 reference

12 December 2020

Turnover of excess hemoglobin alpha chains in beta-thalassemic cells is ATP-dependent

1 reference

12 December 2020

Erythrocyte membrane skeleton abnormalities in severe beta-thalassemia

1 reference

12 December 2020

Cellular and membrane properties of alpha and beta thalassemic erythrocytes are different: implication for differences in clinical manifestations

1 reference

12 December 2020

A study of membrane protein defects and alpha hemoglobin chains of red blood cells in human beta thalassemia

1 reference

12 December 2020

Entrapment of purified alpha-hemoglobin chains in normal erythrocytes. A model for beta thalassemia

1 reference

12 December 2020

Mouse beta thalassemia, a model for the membrane defects of erythrocytes in the human disease

1 reference

12 December 2020

Isolation, characterization, and immunoprecipitation studies of immune complexes from membranes of beta-thalassemic erythrocytes

1 reference

12 December 2020

Biotin labeling as an alternative nonradioactive approach to determination of red cell survival

1 reference

12 December 2020

Oxidation pathways for the intracellular probe 2',7'-dichlorofluorescein

1 reference

12 December 2020

Degradation of Monoubiquitinated .alpha.-Globin by 26S Proteasomes

1 reference

12 December 2020

Thalassaemic erythrocytes: cellular suicide arising from iron and glutathione-dependent oxidation reactions?

1 reference

12 December 2020

Inclusions of hemoglobin erythroblasts and erythrocytes of thalassemia

1 reference

12 December 2020

Identifiers

1 reference

25 January 2017

0 references

1 reference